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Annals of Clinical and Analytical Medicine

E-ISSN: 2667-663X · Monthly · English

Schwartz-Jampel syndrome; A Case Report

Schwartz-jampel syndrome

Abstract

Schwartz-Jampel Syndrome is a rare disease that is characterized with skeletal deformities, joint contractures, and dysmorphic facial appearance. Most patients become
symptomatic within the first decades of life. The diagnosis is based on clinical findings. Movement limitation of joints, delay in starting to walk, and walking with support
are common preliminary findings. The disease is caused by the mutation in heparan sulfate proteoglycan 2 (HSPC2) gene which encodes perlecan protein. Herein we
report a case of Schwartz-Jampel syndrome with the age of 18.

Keywords

schwartz-jampel syndromeskeletal deformityheparan sulfate proteoglycan 2perlecan protein

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How to Cite This Article

Mehmet Balal, Turgay Demir, Filiz Koc. Schwartz-Jampel syndrome; A Case Report. J Clin Anal Med 2018;9(2):168-170. doi:10.4328/JCAM.5515

Publication History

Received:
15.11.2017
Accepted:
29.12.2017
Published Online:
03.01.2018
Printed:
01.03.2018